JScholar Publishers Successful Pregnancy Outcome and Surgical Approach in Women with Re- paired Bladder Exstrophy or Cloacal Exstrophy – Experience from a quater- nary paediatric and adolescent gynaecology centre in Australia
نویسندگان
چکیده
Background: Women with repaired bladder/cloacal exstrophy face unique challenges throughout their pregnancy. Limited obstetric care information available in the current literature. Aims: To review perinatal issues, pregnancy outcomes and surgical techniques for five pregnancies in three women with repaired bladder exstrophy and cloacal exstrophy. Materials and Method Design: A case series and review of the literature. Setting: A quaternary obstetric and paediatric and adolescent gynaecology service in Queensland, Australia. Participants: Women with repaired bladder exstrophy and cloacal exstrophy, managed by the service over a ten-year period from January 2004 to January 2014. Main Outcome Measures: Identification of perinatal and surgical complexities for this cohort of women. Results Antenatal issues in these women with repaired bladder exstrophy or cloacal exstrophy include miscarriage (3/3), malpresentation (3/3), urological complications such as recurrent urinary tract infection (UTI) (3/3), pyelonephritis (1/3), urosepsis (1/3), renal calculi and hydronephrosis (1/3) and stress incontinence (1/3). Other issues identified were hypertension, uterine prolapse, threatened preterm labour, cervical insufficiency, and low lying placenta with antepartum haemorrhage. Surgical planning and foresight of anticipated difficulties at delivery in women with repaired bladder exstrophy and cloacal exstrophy is critical. Conclusions A Women with repaired bladder exstrophy and cloacal exstrophy present additional challenges for those caring for them in the perinatal period. Surgical approach to delivery is best achieved through elective caesarean section with a high midline skin incision to avoid damage to the reconstructed bladder, which overlies the usual transverse suprapubic skin incision made for a lower segment caesarean section.
منابع مشابه
Psychosexual development in genetic males assigned female: the cloacal exstrophy experience.
Genetic males who have cloacal exstrophy, a rare, severe pelvic field defect that leads to aphallia, traditionally have been socially, legally, and surgically sex-assigned female at birth and reared female, despite a male karyotype and a typical male prenatal hormonal milieu. Psychosexual development in such children previously has been unknown. Studies of 29 children revealed that despite the ...
متن کاملCloacal Exstrophy Repair with Primary Closure of Bladder Exstrophy: A Case Report and Review of Literature
Cloacal exstrophy is the most complex congenital, ventral, abdominal wall defect. Traditionally surgery consists of a staged approach to repair which takes place on many separate theatre visits. In this case a primary approach was undertaken resulting in a relatively short inpatient stay and a reduced risk from multiple surgical procedures under general anaesthesia.
متن کاملComplete primary repair of exstrophy.
PURPOSE The surgical correction of bladder exstrophy to achieve continence with voiding remains a challenging problem for the urologist. Since 1989 we have performed complete primary repair for exstrophy based on the concept that the primary defect of bladder and cloacal exstrophy is anterior herniation. Thus, the bladder and urethra must be treated as a single unit to move them posteriorly int...
متن کاملModern Management of the Exstrophy-Epispadias Complex
The exstrophy-epispadias complex is a rare spectrum of malformations affecting the genitourinary system, anterior abdominal wall, and pelvis. Historically, surgical outcomes were poor in patients with classic bladder exstrophy and cloacal exstrophy, the two more severe presentations. However, modern techniques to repair epispadias, classic bladder exstrophy, and cloacal exstrophy have increased...
متن کاملBilateral Anterior Pelvic Osteotomy for Olosure of Bladder Exstrophy: Description of Technique.
Bladder and cloacal exstrophy are rare malformations associated with abnormalities in the pelvis. The objectives in reconstruction are to obtain a closed and continent bladder, with an acceptable cosmetic appearance. Treatment for the abnormalities of pelvic anatomy is an important part of achieving successful treatment for these urological conditions. This article aims to describe the techniqu...
متن کامل